Friday, September 01, 2017

Hailey-Hailey Disease

The patient is a 38 year-old cook with a 14 year history of a pruritic, occasionally painful rash on his torso.  He used triamcinalone cream in the past without relief.  No family history aof a similar process.

O/E.:  There are plaques in axillary folds, on the chest, back, and popliteal fossae.Some advancing borders appear vesicular on close observation.  There is mild post-inflammatory hyperpigmentation in healed sites.

Clinical Photos from L. Axilla:
Laboratory:  An incisional biopsy was taken from the crusted/vesicular edge.

Tentative Diagnosis:  Benign Familial Pemphigus (Hailye-sHaily)

1 comment:

  1. Hi David if the bx is confirmed as Hailey Hailey disease would you consider low dose naltrexone for the treatment ?. Regards Chris Tyson .

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